SESSION TITLE: Thoracic Vascular Disorders
SESSION TYPE: Student/Resident Case Report Slide
PRESENTED ON: Monday, October 24, 2016 at 11:00 AM - 12:00 PM
INTRODUCTION: Tuberous sclerosis complex (TSC) is an autosomal dominant condition that is characterized by hamartomas of viscera and haemangiomas of small blood vessels. Aneurysms of medium/large vessels are rare and have been reported with aorta; renal, brachial, axillary and intracranial arteries. Pulmonary artery (PA) aneurysm itself is very rare on its own. Common etiologies include infection, cardiac and vascular abnormalities including Bechet’s, pulmonary hypertension, and trauma. Less than 5 cases of primary PA aneurysm (PAA) related to TSC have been reported. We are reporting an interesting and to our knowledge, the first reported case of pulmonary vein(PV)/Left atrial(LA) compression by gigantic PAAs associated with TSC.