DISCUSSION: Pulmonary sequestration is a rare finding accounting for about only 5% of congenital pulmonary malformations. It is characterized by dysplastic lung tissue fed by an aberrant artery arising directly from the aorta. In extralobar sequestration, there is a distinct visceral pleura surrounding the dysplastic parenchyma. It is usually diagnosed in vitro, but often does not cause symptoms until adulthood. On imaging, it is commonly seen as a mass because it is rarely aerated. Intralobar sequestration, on the other hand, is more common and is not surrounded by an independent visceral pleura. It is more likely to result in recurrent infection, and therefore, earlier presentation in childhood. Intralobar sequestration imaging shows aerated but abnormal lung tissue. Both forms of sequestration usually require surgical resection due to the risk of massive, life-threatening hemoptysis. Standard thoracotomy or video assisted thoracic surgery (VATS) can be performed. There is limited data but increasing interest in endovascular intervention in adults.