CASE PRESENTATION: This is a 32-year-old female patient, who presented with a 6-month history of persistent upper back pain radiating to the left. A CT-scan, revealed a 3.1 X 2.2 cm left paracardiac mass (Figure 1). The patient was brought to the operating theatre for biopsy and excision of the mass. Upon careful evaluation, the mass was found to be arising from the phrenic nerve which is an atypical site (Figure 2). After multiple unsuccessful attempts to delineate a plane between the nerve and mass, the lesion was resected en bloc with the phrenic nerve. Final pathology demonstrated a partially capsulated yellow adipose tissue measuring 5.5 X 3 X 0.9 cm, with a cellular pattern of dense avascular spindle cell pattern with numerous thin cytoplasmic processes, consistent with Antoni type A cellular pattern. Immunohistochemical analysis demonstrated tissue to be S100 positive and CD34 negative. Paraffin sections were analyzed by immunochemistry and known positive tissues were tested with each antibody and examined to ensure reactivity. These findings were consistent with the diagnosis of schwannoma of the phrenic nerve.