DISCUSSION: IPF is a chronic, progressive fibrosing interstitial pneumonia of unknown cause and associated with histopathologic and/or radiologic pattern of UIP. (1) The mean age at diagnosis is 66 years. It is uncommon in patients younger than 50 years. Historical studies have shown a survival advantage for patients with other forms of IIP when compared to IPF. Our patient presented at a young age with smoking history and bilateral lower lobe predominant reticular opacities favoring a diagnosis of smoking related IIP namely desquamative Interstitial Pneumonia or Respiratory Bronchiolitis - Interstitial lung disease. Sparing of sub-pleural space is characteristic for non-specific interstitial pneumonia. IPF is characterized by peripheral, subpleural reticular opacities with traction bronchiectasis and honeycombing. Biopsy proves pivotal in diagnosis of IIP; which was the case in our patient. Biopsy showed fibroblastic foci which is characteristic for IPF. The treatment of IPF is evolving and changing in recent times with guidelines signifying the role of Pirfenidone and Nintedanib. However, the mortality and survival of this disease entity still remains elusive.