SESSION TITLE: Fellow Case Report Poster - Diffuse Lung Disease II
SESSION TYPE: Affiliate Case Report Poster
PRESENTED ON: Tuesday, October 25, 2016 at 01:30 PM - 02:30 PM
INTRODUCTION: We present a rare case of idiopathic pulmonary fibrosis (IPF) in a 31-year-old patient.
CASE PRESENTATION: A 31 year-old Caucasian male with 20 pack-year smoking history was referred for evaluation of shortness of breath. Symptoms started 6 months ago. It was associated with progressive weight loss and non-productive cough. No occupational exposure. No family history of pulmonary fibrosis. Physical exam showed occasional inspiratory rales. No clubbing. Oxygen saturation was 93% on room air. Chest x-ray showed bilateral symmetric lower lobe nodular interstitial thickening. CT Chest showed bilateral lower lobe predominant reticular thickening and mild traction bronchiectasis with sparing of subpleural space. (Figure 1) Connective tissue work-up was negative. Pulmonary function test showed moderate restriction and moderate decrement in diffusion capacity. Open lung biopsy showed fibroblastic foci with usual interstitial pneumonia (UIP) pattern consistent with IPF. (Figure 2)