In our cohort, we have had examples which contradict the fact that the CT scan pattern of “ground glass opacities in the right middle lobe, lingula, and medial segments of the upper and lower lobes, in the absence of other significant parenchymal abnormalities” is pathognomonic for NEHI. We have managed some patients with clinical chILD and with the same CT scan pattern (Fig 1) as described in NEHI. One case was a 2-year-old girl; another case involved a 6-month-old boy. They also presented with air-trapping, which is another sign of NEHI, both on CT scan and in pulmonary function test results. Both patients improved over years, as expected in NEHI; however, they required corticosteroid therapy, which is unusual in NEHI. In addition, lung biopsy specimens from both patients at diagnosis exhibited a pattern of desquamative interstitial pneumonia with no bombesin-positive pulmonary neuroendocrine cells; this finding is contrary to the diagnosis of NEHI. The patients were both subjected to sequencing of SFTPC, SFTPB, and ABCA3 proteins of surfactant. No genetic mutation was found in the 2-year-old girl, and a single mutation in the ABCA3 protein was found in the 6-month-old boy.