Beijing Anzhen Hospital, Beijing, China
Copyright 2016, American College of Chest Physicians. All Rights Reserved.
SESSION TITLE: Lung Cancer I
SESSION TYPE: Original Investigation Poster
PRESENTED ON: Saturday, April 16, 2016 at 11:45 AM - 12:45 PM
PURPOSE: Pulmonary artery sarcoma (PAS) is an extremely rare and highly malignant tumor of pulmonary artery origin. Since 1923, when the first case was reported by Mandelstamm, no more than 300 cases have been reported worldwide.
METHODS: We report here three cases of PAS who were initially misdiagnosed as PTE or CTEPH, and were later found to be PAS after surgery.
RESULTS: We examined the clinical features of these patients for better diagnosis of PAS in the early stages of the disease because early diagnosis is critical for favorable prognosis for PAS patients.
CONCLUSIONS: PAS has a very poor prognosis, and early diagnosis with radical surgical resection offers PAS patients the only chance of survival.
CLINICAL IMPLICATIONS: Because of its rarity and non-specificity of clinical manifestations and imaging presentation, PAS is frequently misdiagnosed as pulmonary thromboembolic diseases such as pulmonary thromboembolism (PTE) or its late sequel chronic thromboembolic pulmonary hypertension (CTEPH).
DISCLOSURE: Guangfa Zhu: Consultant fee, speaker bureau, advisory committee, etc.: The national natural science foundation
No Product/Research Disclosure Information
Become a CHEST member and receive a FREE subscription as a benefit of membership.
Individuals can purchase this article on ScienceDirect.
Individuals can purchase a subscription to the journal.
Individuals can purchase a subscription to the journal or buy individual articles.
Learn more about membership or Purchase a Full Subscription.
Institutional access is now available through ScienceDirect and can be purchased at myelsevier.com.
Some tools below are only available to our subscribers or users with an online account.
Download citation file:
Web of Science® Times Cited:
Customize your page view by dragging & repositioning the boxes below.
Enter your username and email address. We'll send you a reminder to the email address on record.
Athens and Shibboleth are access management services that provide single sign-on to protected resources. They replace the multiple user names and passwords necessary to access subscription-based content with a single user name and password that can be entered once per session. It operates independently of a user's location or IP address. If your institution uses Athens or Shibboleth authentication, please contact your site administrator to receive your user name and password.