SESSION TITLE: Congenital Disorder Case Report Posters
SESSION TYPE: Case Report Poster
PRESENTED ON: Sunday, March 23, 2014 at 01:15 PM - 02:15 PM
INTRODUCTION: Poland syndrome was first describe by Alfred Poland in 1941, as the presence of syndactyly and the partial or complete absence of ipsilateral chest muscle, although is more common to find absence on its sternocostal portion, with or without absence of the minor pectoral. Pectus excavatum is a congenital deformity of the anterior wall of the thorax, in which the costal cartilages grow abnormally. In previous studies the quantitative evaluation of the lung volume has been reported with scintigraphy with the SPECT-CT technique with 99m Tc macroaggregates formulation, having as a goal to determine the favorable changes of the surgical reconstruction by Thoracoscopy assisted NUSS procedure on patients with pectus excavatum. After the bibliographic review, there were no reports found for the lung function evaluation by the SPECT-CT technique on any thoracic malformation.
CASE PRESENTATION: There are two patients that are 14 and 17 years old, whom present malformations on the rib cage, Poland syndrome and pectus excavatum respectively. They both had lung ventilation/ perfusion scan and SPECT-CT procedure to evaluate their lung function, morphology and perfusion of the affected parenchymal.
DISCUSSION: After the bibliographic review, we didn't found pulmonar scintigraphy with the SPECT-CT technique with 99m Tc macroaggregates, used in patients with toracic malformation to evaluate the pulmonary function, altought that tecnique is used to evaluate the effects after surgical correction.
CONCLUSIONS: Is expected to provide, beside the morphological evaluation by conventional imaging tests, a functional technique with nuclear medicine by the lung ventilation/ perfusion scan with SPECT-CT technique to determine the lung function and changes of the secondary lung parenchymal to congenital alterations of the thoracic cage, keep monitoring and reevaluate the lung function after surgical treatment.
Reference #1: Pearl, Pediatric Radiology Poland Syndrome 1971;101:619-62 2. Pinedo Presentación de un caso de corrección cosmética de pectus excavatum Rev INER 2005;18:117-122 3. Mansour Ann Thorac Surg 2003;76:391-395 4. Protopapas, Journal of Cardiothoracic Surgery 2008,3:40 5. Onur, Ann Saudi Med 2006;26(5):370-374 6. Schanberger, General Thoracic Surgery, 2005 6th ed, Chapter 41
DISCLOSURE: The following authors have nothing to disclose: Sigelinda Sandoval Borrego, Francina Bolanos