Angiosarcomas are very rare and highly malignant sarcomas of vascular endothelial origin, characterized by angiomatous areas of freely anastomosing channels lined by atypical endothelial cells alternating with Kaposi-like spindle cell areas. The mean age at presentation is about 60 years, and there is a slight male preponderance. The most common primary site of involvement is the skin of the head and neck, but other reported sites include the heart, adrenal gland, ovary, prostate, vagina, and maxillary sinus. Factors associated with angiosarcomas include exposure to polyvinyl chloride, thorium dioxide, trauma, and radiation. Reports of association with foreign body, neurofibromatosis, tuberous sclerosis, and meningiomas have been reported. Regardless of their site of origin, angiosarcomas have a striking propensity for lung metastasis. Other frequent sites of metastatic disease include the bone, liver, and lymph nodes.