Follicular dendritic cell sarcoma, as its own entity, is a rare aggressive malignancy of follicular dendritic cells, of which 60% originate from lymph nodes and 40% arise from sites that include the stomach, colon, liver, tonsil, oropharyngeal, and nasopharyngeal areas. Surgical resection with adjuvant chemotherapy is the preferred treatment; however, there is a recurrence rate of 43% and the mortality rate is higher in tumors greater than 6 cm in size and of intraabdominal location. There have been reports of follicular dendritic cell sarcomas developing in association with Castleman disease of the hyaline-vascular type. To our knowledge, there are only three previously reported cases in the literature of PAMS associated with follicular dendritic cell sarcoma without Castleman disease. Only one of these cases reported an association with constrictive bronchiolitis.