The authors report the successful surgical and
chemotherapeutic management of a malignant fibrous histiocytoma with
localization in the heart. This rare malignancy has specific
morphologic characteristics and is diagnosed in adults when it is
already locally aggressive or metastasized. The average survival time
for patients with malignant fibrous histiocytoma is < 12 months.
Neither clinical nor instrumental signs of recurrence have been
detected in this patient after an aggressive surgical resection and a
specific therapeutic approach.