A 3-year-old boy presented with brainstem astrocytoma and central
alveolar hypoventilation syndrome. Contrast MRI of the brain showed
that the tumor involved the cerebellum, with compression of brainstem,
and resolved after surgical resection. Polysomnography performed before
and after total tumor resection showed significant improvement in
nocturnal respiratory rate, respiratory disturbance index, and oxygen
desaturation. It is apparent that central alveolar hypoventilation
syndrome secondary to brainstem tumor may improve after surgical
resection for those with favorable anatomic location and histology.
Serial polysomnography and MRI scans are useful for diagnosis and in
the management plan, and to monitor progress.