Age- and sex-stratified mortality data for cystic fibrosis
(International Classification Disease code 273.0 between 1974 and 1978,
and 277.0 thereafter) were requested from the national offices of
statistics for 16 countries in North America, Western Europe, and
Australasia. In response to these requests, data were provided from the
following 11 countries: Australia (for the years 1974 to 1994), Belgium
(1974 to 1992), England and Wales (1974 to 1994), France (1974 to
1994), Germany (1979 to 1994; West Germany before 1990), the
Netherlands (1974 to 1994), Ireland (1980 to 1994), New Zealand (1974
to 1987), Scotland (1974 to 1994), Sweden (1974 to 1990 alternate
years, 1990 to 1994 all years), and the United States (1974 to 1994).
Data on age at death were available in 1-year age bands for England and
Wales, Ireland, and Scotland; and in 5-year age bands for Belgium, the
Netherlands, Sweden, Australia, New Zealand, and the United States.
Data for France were provided in 10-year age bands, and were used for
visual comparison of trends but were not included in statistical
analysis. To compare international rankings for cystic fibrosis with
those for all cause mortality, we subsequently requested age- and
sex-stratified all-cause mortality data from these countries and were
provided with data in 5-year age bands suitable for comparison with the
cystic fibrosis data from four of them (England and Wales, Scotland,
Ireland, and New Zealand).